Special Edition: eCysticFibrosis Review, Issue 2

CF, Nutrition, and HEMT

Editor's note:

This issue of ePrimaryCare Review is from a sister eLiterature Review series because the content is relevant for primary care providers. By continuing to this activity, you will be redirected to the original eLiterature Review series where you can complete the activity to receive your CME/CEU credits.

In this issue:

Individuals with cystic fibrosis — adults as well infants and children — have long struggled to gain and maintain their weight. But how has the current widespread use of highly effective modulator treatments — HEMT — changed that situation? That’s the focus of this eCysticFibrosis Review Special Edition: CF and Nutrition and HEMT. 

The first part of this program presented an evidence-based Expert Commentary on the current status of weight gain, obesity, and nutrition among people with CF by guest author Katie McDonald, PhD, MS, RDN, CSP, a clinical dietitian at Primary Children's Medical Center in Salt Lake City. The second part is a podcast interview, providing further in-depth discussions between Katie McDonald and three top CF nutrition experts.  

Learning objectives:

  • Describe the current state of overweight and obesity within the adult CF population. 
  • Discuss the impact of highly effective modulator therapy (HEMT) on the nutritional needs of children with CF.  
  • Describe the difference highly effective modulator therapy has had in pregnancy for people with cystic fibrosis. 

Authors:

Katie McDonald, PhD
Katie McDonald, PhD

Clinical Dietitian, Registered Dietitian Nutritionist, Certified Specialist in Pediatrics
Primary Children’s CF Center Outpatient Clinic
Salt Lake City, UT

Megan Gabel, MD
Megan Gabel, MD

Pediatric Gastroenterology Specialist
University of Rochester Medical Center
Rochester, NY

Amanda Leonard, MPH, RD, LD, CDE
Amanda Leonard, MPH, RD, LD, CDE

Advanced Practice Dietitian
Certified Diabetes Care and Education Specialist
Pediatric Nutrition Practitioner
Johns Hopkins Cystic Fibrosis Center
Baltimore, MD

Alexandra Wilson, MS, RDN, CDE
Alexandra Wilson, MS, RDN, CDE

Manager, Cystic Fibrosis Clinical Research Team
National Jewish Health
Denver, CO

Program Directors:

Noah Lechtzin, MD, MHA

Director, Adult Cystic Fibrosis Program
Associate Professor of Medicine
Johns Hopkins University School of Medicine
Baltimore, MD

Peter J. Mogayzel, Jr., MD, PhD

Professor of Pediatrics
Director, Cystic Fibrosis Center
Johns Hopkins University School of Medicine
Baltimore, MD

Donna Peeler, RN

Clinical Nurse 
Pediatric Clinic Coordinator 
Johns Hopkins Cystic Fibrosis Center 
Baltimore, MD

Length of activity:

0.5 hour Physicians
0.5 contact hour Nurses

Launch date: December 23, 2022
Expiration date: December 22, 2024