Special Edition 2025, Issue 1

Cystic Fibrosis Life Transitions

Editor's note:

The “Johns Hopkins Great Strides” team will be walking to raise money to cure cystic fibrosis on May 15th at the Baltimore Zoo. There is currently no cure for cystic fibrosis and too many people with CF die young. I’m walking to help change that reality.

As the dedicated Pediatric and Adult Care Teams work to improve the lives of people with CF and their families, researchers at Johns Hopkins are working to find a cure for this devastating disease. Please help us by joining our team or making a donation. Thank you. For more information, please click here.

In this issue:

Until the advent of highly effective CFTR modulator medications, cystic fibrosis was considered a pediatric disease, because most individuals did not survive into adulthood. Now, with more adults living with CF than children, treatment priorities must change. Clinicians need to increase their understanding of the transitions a longer life with CF entails: from pediatric to adult care; from the possibilities of motherhood and the need for family planning; from adulthood into older age and the infirmities common to all aging adults.

Join us for this Special Edition of eCysticFibrosis Review, as special guest author Dr. Noah Lechtzin, Director of the Adult Cystic Fibrosis Program at the Johns Hopkins University School of Medicine and a long-time eCF Review Program Director, describes the current evidence-based literature to guide clinicians in managing the transitions their patients will need to make as they grow older with their disease. PLUS: To provide a fuller picture, this program contains video commentary of actual patients with CF describing their own transitions.



Learning objectives:

  • Discuss strategies to improve transition from pediatric to adult CF care.
  • Describe evidence about effects of CF and CF DMTs on pregnancy and fertility.
  • Identify recommendations for comorbidity screening in people with CF as they age.
  • Describe tactics to appraise and improve psychologic functioning in people with CF as they age.

Author:

Noah Lechtzin, MD, MHA
Noah Lechtzin, MD, MHA

Director, Adult Cystic Fibrosis Program
Associate Professor of Medicine
Johns Hopkins University School of Medicine
Baltimore, MD

Program Directors:

Noah Lechtzin, MD, MHA

Director, Adult Cystic Fibrosis Program
Associate Professor of Medicine
Johns Hopkins University School of Medicine
Baltimore, MD

Peter J. Mogayzel, Jr., MD, PhD, MBA

Menowitz/Rosenstein Professor of Pediatric Respiratory Sciences
Director, Eudowood Division of Pediatric Respiratory Sciences
Director, Cystic Fibrosis Center
Johns Hopkins School of Medicine
Baltimore, MD 

Donna Peeler, RN, BSN

Senior Clinical Nurse/Case Manager
Pediatric CF Program Coordinator
Johns Hopkins Cystic Fibrosis Center
Baltimore, MD

Length of activity:

1.0 hour Physicians
1.0 contact hour Nurses

Launch date: March 3, 2025
Expiration date: March 2, 2027