Volume 8, Issue 9

In The Clinic: CFTR Modification & Nutritional Deficiencies

Editor's note:

If you’re interested in other valuable CF medical education, our CF Virtual Roundtable webcast is now available on-demand! Start the activity here: virtual.dkbmed.com 

In this program, Peter Mogayzel, Jr., MD, PhD leads a case-based discussion with Patrick Flume, MD and Lisa Saiman, MD on challenges in treating lung infections. Watch as they cover the following topics:

  • Management of patients with declining FEV1
  • Treatment options
  • Reinforcing adherence
  • Working on inhaler techniques
  • Changing inhaled antibiotics
  • Considering a continuous, cycled, or intermittent therapy approach

Interactive monograph also available!

 

In this issue:

The effects of CFTR modifiers on improving lung function in people with cystic fibrosis are well known. But what about their effects on the GI tract that directly affect nutrition?

In this issue, Dr. Michael Wilschanski — Director of Hadassah Hospital’s Pediatric Gastroenterology Unit at Hebrew University in Jerusalem — explains how new findings about CFTR modification can impact clinical practice.

Learning objectives:

  •     Describe the findings that explain the cause of weight gain in patients with CF taking ivacaftor.
  •     Explain how exocrine pancreatic functions may be improved with ivacaftor treatment.

Author:

Michael Wilschanski, MBBS
Michael Wilschanski, MBBS

Director, Pediatric Gastroenterology Unit,
Division of Pediatrics
Hadassah Medical Center, Hebrew University
Jerusalem, Israel

Program Directors:

Peter J. Mogayzel, Jr., MD, PhD

Director, Eudowood Division of Pediatric Respiratory Sciences
Professor of Pediatrics
Director, Cystic Fibrosis Center

Noah Lechtzin, MD, MHA

Director, Adult Cystic Fibrosis Program
Associate Professor of Medicine
Johns Hopkins University School of Medicine
Baltimore, MD

Suzanne Sullivan, RN, BSN

Senior Clinical Nurse
The Johns Hopkins University
Baltimore, MD

Length of activity:

0.5 hour Physicians
0.5 contact hour Nurses

Launch date: June 21, 2019
Expiration date: June 20, 2021